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Primary immunodeficiency diseases : definition, diagnosis, and management /

Primary immunodeficiency diseases : definition, diagnosis, and management / Nima Rezaei, Asghar Aghamohammadi, Luigi Notarangelo, eds. - xxviii, 358 pages : illustrations ; 26 cm

Includes bibliographical references and index.

Introduction on Primary Immunodeficiency Diseases.- Combined T- and B-Cell Immunodeficiencies.- Predominantly Antibody Deficiencies.- Phagocytes Defects.- Genetic Disorders of Immune Regulation.- Defects in Intrinsic and Innate Immunity: Receptors and Signaling Components.- Autoinflammatory Disorders.- Complement Deficiencies.- Other Well-Defined Immunodeficiencies.- Syndromic Immunodeficiencies.


9783540785378 (alk. paper) 354078537X (alk. paper) 9783540789369 (eISBN) 3540789367 (eISBN)

2008932110


Immunological deficiency syndromes.
Immunological deficiency syndromes--Diagnosis.
Immunological deficiency syndromes--Treatment.
Immunologic Deficiency Syndromes--diagnosis.
Genetic Diseases, Inborn--diagnosis.
Genetic Diseases, Inborn--therapy.
Immunologic Deficiency Syndromes--therapy.

RC606 / .P747 2008

616.079 / P