TY - BOOK AU - Rezaei,Nima AU - Notarangelo,Luigi AU - Aghamohammadi,Asghar TI - Primary immunodeficiency diseases: definition, diagnosis, and management SN - 9783540785378 (alk. paper) AV - RC606 .P747 2008 U1 - 616.079 22 PY - 2008///] CY - Berlin PB - Springer KW - Immunological deficiency syndromes KW - Diagnosis KW - Treatment KW - Immunologic Deficiency Syndromes KW - diagnosis KW - Genetic Diseases, Inborn KW - therapy N1 - Includes bibliographical references and index; Introduction on Primary Immunodeficiency Diseases.- Combined T- and B-Cell Immunodeficiencies.- Predominantly Antibody Deficiencies.- Phagocytes Defects.- Genetic Disorders of Immune Regulation.- Defects in Intrinsic and Innate Immunity: Receptors and Signaling Components.- Autoinflammatory Disorders.- Complement Deficiencies.- Other Well-Defined Immunodeficiencies.- Syndromic Immunodeficiencies UR - http://repository.fue.edu.eg/xmlui/handle/123456789/1647 ER -